Associated Anomaly of Esophageal Atresia.
- Author:
Jino BAEK
1
;
Eunyoung JUNG
;
Woo Hyun PARK
;
Soon Ok CHOI
Author Information
1. Department of Pediatric Surgery, Dongsan Medical Center, Keimyung University School of Medicine, Daegu, Korea. choi1635@dsmc.or.kr
- Publication Type:Original Article
- Keywords:
Tracheoesophageal fistula;
Esophageal atresia;
Congenital abnormalites
- MeSH:
Benzeneacetamides;
Demography;
Ductus Arteriosus, Patent;
Esophageal Atresia;
Extremities;
Female;
Heart Septal Defects, Atrial;
Heart Septal Defects, Ventricular;
Humans;
Infant, Newborn;
Male;
Piperidones;
Tracheoesophageal Fistula
- From:Journal of the Korean Association of Pediatric Surgeons
2011;17(1):81-87
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
This study was aimed to evaluate associated congenital anomalies in the patients with esophageal atresia with tracheoesophageal fistula (EA/TEF). Forty-two neonates with the diagnosis of EA/TEF treated over a 10 year period in a single institution were included in this study. The demography of EA/TEF was analyzed. Major associated anomalies including vertebral, anal, cardiac, renal, limb, neurologic and chromosome were reviewed and categorized. Males were slightly more dominant than females (1.47:1) and all patients had Gross type C EA/TEF. Only 19% of the patients had solitary EA/TEF without associated anomalies. Cardiac anomalies were the most common associated congenital anomaly in patients with EA/TEF (73.8%). But 47.6% were cured spontaneously or did not affect patients' life. Atrial septal defect (ASD) was the most common cardiac anomaly followed by patent ductus arteriosus (PDA) and ventricular septal defect (VSD). Among gastrointestinal anomalies (23.8%), anorectal malformations were the most frequent, 70% Vertebral and limb abnormalities accounted for 11.9% and urogenital malformations 9.5% of the anomalies in patients with EA/TEF. VACTERL associated anomalies were 23.8% and 4.8% had full VACTERL. Almost 12% of EA/TEF had neurologic anomalies. Patients with EA/TEF require preoperative evaluation including neurologic evaluation to detect anomalies not related to VACTERL. Though associated cardiac anomaly occurred in 73.8% of patients in our study, only 21.42% needed surgical correction. The authors suggesrs further studies with large numbers of patients with EA/TEF.
