A case of testicular adrenal rest tumor in a male child with congenital adrenal hyperplasia.
10.3345/kjp.2008.51.9.1018
- Author:
Joo Hwa KIM
1
;
Kyong Ah YUN
;
Choong Ho SHIN
;
Sei Won YANG
Author Information
1. Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea. chshinpd@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Testicular neoplasms;
Adrenal rest tumor;
Child;
Congenital adrenal hyperplasia;
Steroid;
21-hydroxylase
- MeSH:
Adrenal Hyperplasia, Congenital;
Adrenal Rest Tumor;
Child;
Humans;
Male;
Orchiectomy;
Steroid 21-Hydroxylase;
Testicular Neoplasms
- From:Korean Journal of Pediatrics
2008;51(9):1018-1022
- CountryRepublic of Korea
- Language:English
-
Abstract:
Testicular adrenal rest tumors are a well-known complication in male patients with congenital adrenal hyperplasia. Corticosteroid suppressive therapy usually results in the regression of these tumors. We describe a patient with 21-hydroxylase deficiency who developed bilateral testicular masses. Despite steroid suppressive therapy, the tumors did not regress and hormonal control was poor. Consequently, bilateral partial orchiectomies were performed.
