Histiocytosis-X with Giant Occipital Scalp Mass: A Case Report.
- Author:
Yong Sung LEE
1
;
Si Hun SONG
;
Seong Ho KIM
;
Kwan Tae KIM
;
Youn KIM
Author Information
1. Department of Neurosurgery, College of Medicine, Chungnam National University, Taejeon, Korea.
- Publication Type:Original Article
- Keywords:
Histiocytosis-X;
Eosinophilic granuloma;
Hand-Schuller-Christian disease;
Letterer-Siwe disease
- MeSH:
Drug Therapy;
Eosinophilic Granuloma;
Granulation Tissue;
Granuloma;
Histiocytosis;
Histiocytosis, Langerhans-Cell*;
Humans;
Infant;
Mononuclear Phagocyte System;
Rare Diseases;
Scalp*;
Skull
- From:Journal of Korean Neurosurgical Society
1993;22(9):1022-1025
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Histiocytosis is a relatively rare disorder of the reticuloendothelial system involving the proliferation of histicoytes, granulation tissue, and inflammatory cells in many different organ systems1). Thus, the three manifestations of the same basic pathologic process:Eosinophilic granuloma, Hand-Schuller-Christian disease, and Letterer-Siwe disease have been classified as localized, chronic disseminated and acute disseminated histiocytosis-X. They were therefore included under the term histiocytosis-X and this concept has been generally accepted. The authors have experienced one case of histiocytosis-X, a rare disease. A 11 month-old femal patient presented with gradually enlarged palpable mass on the occipital area. The occipital skull was defected in a punched out fashion. The mass was completely removed. The pathologic findings revealed Histiocytosis-X and the patient was given chemotherapy.
