Interrupted Aortic Arch with Apical Muscular Ventricular Septal Defect Associating Esophageal Atresia with Tracheoesophageal Fistula.
- Author:
Si Chan SUNG
1
;
Jeong Su CHO
;
Hyoung Doo LEE
Author Information
1. Department of Thoracic and Cadiovascular Surgery, College of Medicine, Pusan National University, Busan, Korea. scsung@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Aortic arch, interrupted;
Heart septal defect, ventricular;
Esophageal stresia;
Tracheoesophageal fistula;
Aortic arch
- MeSH:
Airway Obstruction;
Aorta, Thoracic*;
Esophageal Atresia*;
Heart Septal Defects, Ventricular*;
Humans;
Infant, Newborn;
Pulmonary Artery;
Pyloric Stenosis, Hypertrophic;
Thoracotomy;
Tracheoesophageal Fistula*
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2004;37(10):856-860
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Interrupted aortic arch with concomitant intracardiac defects is a rare congenital anomaly that has an unfavorable natural course. We report a successful staged operation of interrupted aortic arch with apical muscular ventricular septal defect associating esophageal atresia with tracheoesophageal fistula in a 3-day-old neonate weighing 2.6 kg. We repaired esophageal atresia through the right thoracotomy and subsequently performed extended end-to-end anastomosis of the aortic arch with pulmonary artery banding through the left thoracotomy at same operation. The apical muscular VSD was repaired 87 day after first operation. The patient required multiple additional interventions before closure of the apical muscular ventricular septal defect, such as pyloromyotomy for idiopathic hypertrophic pyloric stenosis, anterior aortopexy for airway obstruction, and balloon aortoplasty for residual coarctation. She is now doing well.
