Hereditary Sclerosing Poikiloderma.
10.3346/jkms.2012.27.2.225
- Author:
Hyo Jin LEE
1
;
Dong Hoon SHIN
;
Jong Soo CHOI
;
Ki Hong KIM
Author Information
1. Department of Dermatology, College of Medicine, Yeungnam University, Daegu, Korea. dhshin@med.yu.ac.kr
- Publication Type:Case Reports
- Keywords:
Hereditary Sclerosing Poikiloderma;
Korean
- MeSH:
Abnormalities, Multiple;
Adolescent;
Elastic Tissue/pathology;
Fingers/abnormalities;
Humans;
Hyperpigmentation/pathology;
Male;
Micrognathism/pathology;
Rothmund-Thomson Syndrome/*diagnosis/pathology;
Sclerosis/pathology;
Skin Diseases/diagnosis/pathology
- From:Journal of Korean Medical Science
2012;27(2):225-227
- CountryRepublic of Korea
- Language:English
-
Abstract:
Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
