A Case of Anterior Lenticonus in Alport's Syndrome.
- Author:
Hee La LEE
1
;
Mi Ri RHEE
;
Yoon Bo SHIM
;
Bong Chul KIM
Author Information
1. Department of Ophthalmology, School of Medicine, Soon Chun Hyang University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Alport's syndrome;
Anterior lenticonus;
Hemorrhagic Nephritis;
Deafness
- MeSH:
Anterior Chamber;
Deafness;
Hematuria;
Humans;
Nephritis;
Nephritis, Hereditary*;
Proteinuria;
Young Adult
- From:Journal of the Korean Ophthalmological Society
1989;30(2):305-309
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Alport's syndrome, first described by Alport in 1927, is a clinical entity which consists of lens abnormalities, hereditary hemorrhagic nephritis and nerve deafness. Anterior lenticonus is a rare structual anomaly of lens in which there is a conicalor spherical protrusion of the anterior lens surface into the anterior chamber as a characteristic finding of Alport's syndrome. The authers experienced a case of Alport's syndrome in a 22-year-old man associated with bilateral anterior and posterior lenticonus, hematuria, proteinuria, renal failur earld nerve deafness(complete form).
