A Case of Aortic Dissection with Marfan Syndrome and Ankylosing Spondylitis.
- Author:
Ji Won RYOU
1
;
Ji Young PARK
;
Eun Ju SONG
;
Jin Wuk HUR
Author Information
1. Department of Internal Medicine, Eulji University College of Medicine, Seoul, Korea. rheumatism@eulji.ac.ar
- Publication Type:Case Report
- Keywords:
Marfan syndrome;
Aortic dissection;
Ankylosing spondylitis
- MeSH:
Abdominal Pain;
Arachnodactyly;
Arm;
Back Pain;
Blood Pressure;
Butanones;
Humans;
Male;
Marfan Syndrome;
Mass Screening;
Microfilament Proteins;
New York;
Pelvis;
Sacroiliitis;
Spine;
Spondylitis, Ankylosing;
Sulfasalazine
- From:Korean Journal of Medicine
2013;84(6):873-877
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 33-year-old male presented with an acute onset of back pain and abdominal pain. He was 189.9 cm tall and had an arm span of 194 cm, and had mild pectus carinatum as well as arachnodactyly. Plain radiographs showed kyphoscoliosis of the lumbar spine, bamboo spine of the thoracic spine, and sacroiliitis of the pelvis. Abdominal computed tomography revealed debakey type 3 aortic dissection. We prescribed beta blockers to control his blood pressure. According to the modified New York criteria, we diagnosed him with HLA negative ankylosing spondylitis and initiated therapy with nabumetone and sulfasalazine. We later diagnosed Marfan syndrome based on the Ghent criteria and mutation screening at the fibrillin-1. After treatment, he has been followed up without symptoms or complications.
