Malignant Transformation of Fibrous Dysplasia on Anterior Skull Base.
- Author:
Chul Jae LEE
1
;
Seong Min KIM
Author Information
1. Department of Neurosurgery, Kosin University College of Medicine, Busan, Korea.
- Publication Type:Case Report
- Keywords:
Fibrous dysplasia;
Skull base;
Malignant transformation
- MeSH:
Fibrous Dysplasia, Polyostotic;
Incidence;
Neurologic Manifestations;
Orbit;
Skull Base*;
Skull*
- From:Journal of Korean Neurosurgical Society
2005;37(5):383-385
- CountryRepublic of Korea
- Language:English
-
Abstract:
Malignant transformation of fibrous dysplasia is a rare condition and the incidence is estimated at 0.4% for fibrous dysplasia and 4% for Albright's syndrome. The authors did not find a reported case of malignant change at skull base around the orbit in the literature. We experienced a case of fibrous dysplasia, in which neurologic symptoms were aggravated due to malignant change around the orbit, and report its favorable outcome obtained with total surgical removal.