Diffuse pulmonary lymphangiomatosis: a case report with literature review.
- Author:
Ming-Hua DU
1
;
Ruan-Jian YE
;
Kun-Kun SUN
;
Jian-Feng LI
;
Dan-Hua SHEN
;
Jun WANG
;
Zhan-Cheng GAO
Author Information
1. Department of Respiratory & Critical Care Medicine, Beijing University People's Hospital, Beijing 100044, China.
- Publication Type:Case Reports
- MeSH:
Bronchoscopy;
Female;
Humans;
Lung Diseases;
congenital;
diagnosis;
diagnostic imaging;
metabolism;
Lymphangiectasis;
congenital;
diagnosis;
diagnostic imaging;
metabolism;
Middle Aged;
Tomography, X-Ray Computed
- From:
Chinese Medical Journal
2011;124(5):797-800
- CountryChina
- Language:English
-
Abstract:
Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes a progressive clinical course, eventually causing deterioration of the lung. Both the clinical diagnosis and treatment of DPL remain a challenge. Here, we report a case of DPL in a 53-year-old Chinese woman with comprehensive investigations including pulmonary function tests, computer tomography (CT), bronchoscopy and histological examination of the lung biopsy, and review the literature.
