Persistent Müllerian duct syndrome: a report of 2 cases and review of the literature.
- Author:
Xiao-Bing JU
1
;
Wei ZHANG
;
Hong-Fei WU
;
Li-Xin QIAN
;
Bai-Xin SHEN
;
Zheng-Quan XU
;
Yuan-Geng SUI
Author Information
- Publication Type:Case Reports
- MeSH: Adult; Disorders of Sex Development; pathology; Follow-Up Studies; Humans; Male; Mullerian Ducts; abnormalities; Syndrome
- From: National Journal of Andrology 2008;14(1):51-54
- CountryChina
- Language:Chinese
-
Abstract:
OBJECTIVETo study the etiopathogenesis, clinical manifestations, diagnosis and management of persistent Müllerian duct syndrome (PMDS).
METHODSTwo cases of PMDS were reported, one accompanied by transverse testicular ectopia and the other associated with cryptorchidism. Corporeal hysterectomy and orchidopexy were given to both the patients and cryptorchidectory the latter.
RESULTSVascular supply and texture of the testis were normal in both the 2 patients after 1.5-2 years' follow-up.
CONCLUSIONPMDS is male pseudohermaphroditism, for which means should be taken to preserve the blood supply and fertility function of the testis in surgical management, and attention should be paid to possible development of testis tumor in follow-up.