Secondary Glaucoma in Neurofibromatosis with Non-Pigmented Nodules of the Iris, Ectropion Uveae and Buphthalmos.
- Author:
Kong Sup KWAK
1
;
Kyoo Won LEE
Author Information
1. Department of Ophthalmology, Yeungnam University, College of Medicine, Daegu, Korea.
- Publication Type:Case Report
- MeSH:
Child;
Ectropion*;
Female;
Glaucoma*;
Humans;
Hydrophthalmos*;
Iris*;
Neurofibroma, Plexiform;
Neurofibromatoses*;
Skin;
Uvea*
- From:Journal of the Korean Ophthalmological Society
1986;27(4):709-715
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Neurofibromatosis (von Recklinghausen's disease) involves the eye in a great variety of clinical appearances. Secondary glaucoma with congenital ectropion uveae and mild buphthalmos in one eye and non-pigmented nodules in the iris of both eyes were observed in a 9-year-old girl with generalized neurofibromatosis. The patient also exhibited pigmented patches (cafe-au-lait spots) and multiple nodular masses of the skin. Two of the masses were excised and vitrified as plexiform neurofibroma, microscopically. This paper reports clinical, biomicroscopic, ophthalmoscopic, gonioscopic and histological findings in the patient.
