A Case of Gronblad-Strandberg Syndrome.
- Author:
Ki Cheol KWAK
1
;
Jae Duck KIM
Author Information
1. Department of Ophthalmology, Won-Kwang University, School of Medicine, Iri. Korea.
- Publication Type:Case Report
- MeSH:
Adult;
Angioid Streaks;
Axilla;
Basophils;
Calcium;
Dermis;
Elastic Tissue;
Female;
Fluorescein Angiography;
Humans;
Neck;
Ophthalmoscopy;
Optic Disk;
Pseudoxanthoma Elasticum*;
Skin
- From:Journal of the Korean Ophthalmological Society
1986;27(4):729-734
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pseudoxanthoma elasticum associated with angioid streaks has been called rthe Gronblad-Strandberg Syndrome. A 30-year-old female patient showed circumscribed, cream-colored, crepelike, redundant plaques on neck, axillae, periumbilical area, and inguinal regions. The histopathologic findings of the skin taken from the axilla revealed extensive basophilic degeneration of the elastic tissue and calcium deposition in the middle and lower dermis. Both fundi showed irregular angioid streaks radiating from the optic disk on ophthalmoscopy, and hyperfluorescence of angioid streaks was noted with fluorescein angiography.
