A Pathology-proven Case of Schilder's Disease.
- Author:
Byung Su KIM
1
;
Byoung Joon KIM
;
Kwang Ho LEE
;
Gyeong Moon KIM
Author Information
1. Department of Neurology, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. kimgm@skku.edu
- Publication Type:Case Report
- Keywords:
Diffuse sclerosis;
Demyelinating disease;
White matter
- MeSH:
Aged;
Demyelinating Diseases;
Diffuse Cerebral Sclerosis of Schilder;
Female;
Humans;
Multiple Sclerosis
- From:Journal of the Korean Neurological Association
2008;26(1):50-54
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Schilder's disease or myelinoclastic diffuse sclerosis (MDS) is a rare variant of multiple sclerosis. We report a 66-year-old woman with progressive motor weakness and diffuse white matter degeneration on MRI, which satisfies the Poser's restrictive criteria of MDS. As previously reported cases of probable Schilder's disease did not meet the criteria correctly, we consider our patient is the first pathology-proven case of MDS in Korea.
