Maffucci's Syndrome Associated with Chondrosarcoma and Aneurysm: Case Report.
10.3348/jkrs.2002.47.6.557
- Author:
Hyoung Gun LIM
1
;
Won Jong YOO
;
Yeon Soo LIM
;
Mi Sook SUNG
;
Myung Hee CHUNG
;
Hae Giu LEE
;
So Lyung JUNG
;
Jea Na KIM
Author Information
1. Department of Radiology, College of Medicine, The Catholic University of Korea, Korea. wjyu@hfh.cuk.ac.kr
- Publication Type:Case Report
- Keywords:
Maffucci syndrome;
Enchondroma;
Hemangioma;
Chondrosarcoma;
Aneurysm, intracranial
- MeSH:
Aneurysm*;
Chondroma;
Chondrosarcoma*;
Enchondromatosis;
Hemangioma;
Intracranial Aneurysm;
Mesoderm
- From:Journal of the Korean Radiological Society
2002;47(6):557-560
- CountryRepublic of Korea
- Language:English
-
Abstract:
Maffucci syndrome is a rare congenital non-inherited condition characterized by multiple enchondromas and cutaneous hemangiomas. It is associated with increased risk of malignancy, including chondrosarcomas, and because of generalized mesodermal dysplasia, aneurysms can develop. We present a case of Maffucci syndrome associated with intracranial chondrosarcoma and aneurysm.