Erythrokeratodermia Variabilis with Alopecia Universalis.
10.5021/ad.1990.2.1.17
- Author:
Jong Seung LEE
;
Yeul Hoon SUNG
;
Jeung Hoon LEE
;
Jang Kyu PARK
- Publication Type:Original Article
- Keywords:
Alopecia universalis;
Erythrokeratodermia variabilis;
Etretinate;
Ichthyosiform dermatosis
- MeSH:
Acitretin;
Alopecia*;
Child;
Diagnosis;
Erythrokeratodermia Variabilis*;
Etretinate;
Extremities;
Female;
Humans
- From:Annals of Dermatology
1990;2(1):17-20
- CountryRepublic of Korea
- Language:English
-
Abstract:
We describe a 8-year-old girl with erythrokeratodermia varibilis (EKV). This diagnosis was supported by erythematous, configurate patches over the entire body. Their size, shape and location varyed with enviromental factors and emotional state. In addition, well defined brownish, hyperkeratotic plaques were scattered over the trunk and extremities. Also, this patient had alopecia universalis, which is not typical of EKV. Etretinate therapy resulted in an almost complete clinical clearing of the plaques; however, her alopecia universalis and erythematous lesions were not affected.