Pulmonary Lymphangioleiomyomatosis with Chylous Pleural Effusion.
10.4046/trd.2001.50.1.127
- Author:
Byung Joon PARK
;
Jae Hwa CHO
;
Tae Hoon MOON
;
Sang Joon PARK
;
Jung Seon RYU
;
Hong Lyeol LEE
;
Seung Min KWAK
;
Chul Ho CHO
- Publication Type:Case Report
- Keywords:
Lymphangioleiomyomatosis;
Chylous pleural effusion
- MeSH:
Adult;
Biopsy;
Female;
Humans;
Lung;
Lymphangioleiomyomatosis*;
Myocytes, Smooth Muscle;
Pleural Effusion*
- From:Tuberculosis and Respiratory Diseases
2001;50(1):127-131
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Pulmonary lymphangioleiomyomatosis is a disease involving the proliferation of atypical smooth muscle cells trom the perilymphatics, peribronchial and perivascular region of the lung and the retroperitneum. The disease usually affects women of child-bearing age. We recently experienced a case of pulmonary lymphangioleiomyomatosis in a 31-year-old women who had suffered from a chylous pleural effusion. Histologic confirmation of lymphangioleiomyomatosis was made upon a video-associated thoracoscopic lung biopsy. Here we report this case with a brief review of the literature.