Moyamoya Disease in Childen.
- Author:
Hyun Jong CHIN
;
Jun Su LEE
;
Chang Jun COE
- Publication Type:Original Article
- MeSH:
Brain;
Carotid Artery, Internal;
Cerebral Angiography;
Child;
Circle of Willis;
Constriction, Pathologic;
Female;
Frontal Lobe;
Hemorrhage;
Humans;
Infarction;
Male;
Moyamoya Disease*;
Paresis;
Seizures;
Sex Distribution;
Vascular Diseases
- From:
Journal of the Korean Child Neurology Society
1997;5(1):119-125
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: Moyamoya disease is a primary vascular disease characterized by stenosis that is followed by occlusion of the intracranial portion of the internal carotid artery and other vessels of the circle of Willis. Since there has not been any specific reports about clinical manifestation in children, we plan to study on clinical manifestation through these patients who have moyamoya disease. METHODS: We have reviewed our case of moyamoya disease in patients admitted to Yonsei University College of Medicine and analyzed their age & sex distribution as well as clinical manifestations, together with brain CT and angiographic findings. RESULTS: The results were as follows: 1) Fifty cases of moyamoya disease were encounted during a 10-year period. 2) The male to female ratio was 1:2.3 and mean age was 6.3 years old. 3) The most common chief complaint on admission was hemiparesis followed by convulsion. 4) 42 patients(84%) showed infarction on brain CT and only 5 patients(10%) showed hemorrhage. Most common lesion was frontal lobe. 5) Bilateral occlusion of the internal carotid arteries was most common site of lesions on cerebral angiography.
