A Case of Orbital Rhabdomyosarcoma.
- Author:
Kyu Hong PAK
1
;
Moon Ja CHO
;
San Moon CHUNG
;
Nam Ho BEAK
Author Information
1. Department of Ophthalmology, Catholic University Medical College, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
rhabdomyosarcoma;
proptosis;
hematoma;
rhabdoblasts;
cross-striation
- MeSH:
Child;
Cytoplasm;
Drainage;
Drug Therapy;
Exophthalmos;
Giant Cells;
Hematoma;
Humans;
Male;
Orbit*;
Rhabdomyosarcoma*;
Rhabdomyosarcoma, Embryonal;
Tomography, X-Ray Computed
- From:Journal of the Korean Ophthalmological Society
1990;31(5):691-695
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The orbital rhabdomyosarcoma is the most common primary malignant tumor of the orbit in childhood. It was first described in 1854 by Weber and has been increased possibly due to improvement of diagnostic procedures. A 7-year-old boy with the complaints of proptosis and visual disturbance coincidently had an ocular trauma. Incision and drainage of intraorbital hematoma was performed in the right orbit which was confirmed with orbital CT scan. Microscopic findings showed ovoid and spindle shaped rhabdoblasts, hyperchromatic nuclei, and characteristic cross striation in the cytoplasm of the giant cells. He was diagnosed as embryonal rhabdomyosarcoma. The intraorbital hematoma and surrounding tissue in the right orbit were excised and the right eye was enucleated. He received chemotherapy and radiation therapy.
