A Congenital Giant Hepatic Hemangioendothelioma Treated with Interferon-alpha and Complete Tumor Resection.
- Author:
Min A CHO
1
;
Jae Eun YU
;
Moon Sung PARK
;
Jun Eun PARK
;
Jeong HONG
;
Young Bae KIM
Author Information
1. Department of Pediatrics, Ajou University School of Medicine, Suwon, Korea. jeyumd@ajou.ac.kr
- Publication Type:Case Report
- Keywords:
Infantile hepatic hemangioendothelioma;
Interferon-alpha
- MeSH:
Disseminated Intravascular Coagulation;
Heart Failure;
Hemangioendothelioma;
Hemorrhage;
Interferon-alpha
- From:Journal of the Korean Society of Neonatology
2008;15(2):183-189
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Infantile hepatic hemangioendotheliomas (IHHEs) are benign vascular tumors, but can be associated with the life-threatening complications, such as congestive heart failure, disseminated intravascular coagulation, and massive bleeding. Various therapeutic options have been developed and the treatment response depends on the patient's clinical status and the nature of the lesion. In the case of a symptomatic IHHE, a non-invasive and precise diagnosis should be performed promptly before the therapeutic method is chosen. Additionally, it should be kept in mind that the residual lesions have malignant potential. We report a case of a congenital giant IHHE that was successfully reduced in size by interferon-alpha and completely removed by surgical tumor resection with a hepatic lobectomy.
