Two Cases of 2:1 Atrioventricular Block in Infants with Idiopathic Long QT Syndrome.
- Author:
In Jeong KIM
1
;
Byung Ju KIM
;
Jae Sook MA
Author Information
1. Department of Pediatrics, Yosu Chonnam Hospital, Yosu, Korea.
- Publication Type:Case Report
- Keywords:
Long QT syndrome;
2:1 AV block;
Infant
- MeSH:
Arrhythmias, Cardiac;
Atrioventricular Block*;
Child;
Death, Sudden;
Female;
Follow-Up Studies;
Humans;
Infant*;
Infant, Newborn;
Long QT Syndrome*;
Parturition;
Propranolol;
Seizures;
Syncope;
Tachycardia, Ventricular
- From:Journal of the Korean Pediatric Society
1999;42(9):1317-1321
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Idiopathic long QT syndrome(LQTS) is an important cause of syncope, seizures, serious ventricular arrhythmias and sudden death in children. The abnormalities of AV conduction such as 2:1 AV block in children with LQTS is rarely reported. We reported two cases of 2:1 atrioventricualr block in infants with LQTS. Patient 1, a female newborn, revealed bradycardia(60 beats/min) and QTc of 0.65sec with 2:1 AV block at birth. She died of polymorphic ventricular tachycardia at 26days of age. Patient 2, a 2-month-old female, exhibited prolonged QT interval (QTc=0.54sec), 2:1 AV block, and intermittent Wenckebach conduction. After she received propranolol, sinus rhythm with 1:1 AV conduction and QTc of 0.5sec was seen. After a follow-up of 6 months, the infant is still doing well.
