Endolymphatic sac papillary tumor: a case report.
- Author:
Shun-Jiang YU
1
;
Yi-Dong CHEN
;
Feng GAO
;
Xiao-Guang QIU
;
Hong CHANG
Author Information
1. Department of Radiation Oncology, Beijing Shijitan Hospital & Peking University No. 9 Clinical College, Beijing 100038, China. yushunjiang@yahoo.com
- Publication Type:Case Reports
- MeSH:
Adult;
Ear Neoplasms;
diagnostic imaging;
pathology;
surgery;
Endolymphatic Sac;
diagnostic imaging;
pathology;
surgery;
Female;
Humans;
Radiography
- From:
Chinese Medical Journal
2011;124(22):3828-3829
- CountryChina
- Language:English
-
Abstract:
Endolymphatic sac papillary tumor (ELST) is an extremely rare and aggressive tumor characterized by hearing loss and temporal bone destruction. A case with clinical, imaging, pathologic and treatment data is reported and relevant literature is reviewed. A 25-year-old woman, with ELST underwent craniotomy for tumor subtotal resection, and the diagnosis was confirmed by pathologic examination. Postoperative radiotherapy consisted of 50.4 Gy/28 f was given accordingly. The patient is currently alive with no signs of tumor recurrence locally and no radiation side-effects observed after one year follow-up. Complete resection is impossible in most cases, local resection, adjuvant radiotherapy may provide favored local control. A long-term follow-up is highly advocated in consideration of its slow development course.