Adrenocorticotropic hormone-producing pheochromocytoma: a case report and review of the literature.
- Author:
Xun-gang LI
1
;
Dong-xu ZHANG
;
Xiang LI
;
Xin-gang CUI
;
Dan-feng XU
;
Yao LI
;
Yi GAO
;
Lei YIN
;
Ji-zhong REN
Author Information
1. Department of Urologic Surgery, Affiliated Changzheng Hospital of the Second Military Medical University, Shanghai 200003, China.
- Publication Type:Case Reports
- MeSH:
Adolescent;
Adrenal Gland Neoplasms;
diagnosis;
secretion;
therapy;
Adrenocorticotropic Hormone;
secretion;
Female;
Humans;
Pheochromocytoma;
diagnosis;
secretion;
therapy
- From:
Chinese Medical Journal
2012;125(6):1193-1196
- CountryChina
- Language:English
-
Abstract:
Ectopic Cushing’s syndrome caused by pheochromocytoma is rare. We reported a 15-year-old female patient who was admitted to hospital with typical Cushing’s syndrome. She had not started menstruation. Her plasma adrenocorticotropic hormone (ACTH) and 24-hour urinary free cortisol levels were extremely high. Gonadal and progestational hormone levels were also abnormal. Abdominal computed tomography scans and enhanced scans revealed multiple irregular tumors in the right adrenal. Pelvic echogram showed an infantile uterus, while the ovaries were at an immature stage of development. Retroperitoneal laparoscopic right adrenalectomy was performed without intraoperative complications. Histology and immunohistochemistry of the tumor were consistent with pheochromocytoma. Retroperitoneal laparoscopic adrenalectomy is a safe procedure with satisfactory outcomes and allows for rapid recovery.
