Experience of Single Stage Treatment of Caniosynostosis, Hypertelorism, Exophthalmos Patient.
- Author:
Chul Hoon CHUNG
1
;
Seok Chan EUN
;
Dong Kuk SEO
;
Woo Sung JO
;
Se Hyuck PARK
Author Information
1. Department of Plastic and Reconstructive Surgery, Hallym University College of Medicine, Seoul, Korea. c21ps@hallym.or.kr
- Publication Type:Case Report
- Keywords:
Craniosynostosis;
Hypertelorism;
Exophthalmos
- MeSH:
Child;
Congenital Abnormalities;
Craniosynostoses;
Craniotomy;
Exophthalmos*;
Humans;
Hypertelorism*;
Male;
Orbit;
Skull Base;
Surgical Procedures, Operative;
Sutures;
Synostosis
- From:Journal of the Korean Society of Plastic and Reconstructive Surgeons
2006;33(2):237-240
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The simultaneous correction of the hypertelorism and exophthalmos combined with craniosynostosis is very rarely performed operative procedures in the world. The craniosynostosis is the congenital anomaly that designates premature fusion of one or more sutures in either cranial vault or cranial base. Hypertelorism is not a distinct clinical syndrome in itself, but is a physical finding secondary to facial and cranial maldevelopment and it is defined as a increase in the distance between the medial orbital walls. Exophthalmos can occur following the decrease in the size of the orbit in patients with developmental skeletal disorders such as craniofacial synostosis. The authors experienced 9-year-old male patient, who has complex cranio-facial abnormality. The craniosynostosis was oxycephaly type and primary fronto-orbital advancement surgery had been performed in other hospital. The abnormal cranial vault combined with hypertelorism and exophthalmos due to maldeveloped both orbital walls. Surgical correction was obtained by various cranio-fronto-orbital remodeling technique such as calvarial bone craniotomy, fronto-orbital advancement, paramedian resection, medial canthopexy, Tessier-Wolfe three wall orbital expansions. We achieved a quite satisfactory result both functionally and aesthetically in a complex cranio-facial deformity patient by combination and modification of previously developed various cranio-facial plasty technique and hereby report the case with brief discussion and review of literature.
