Systemic mononuclear inflammatory vasculopathy associated with Sjogren's syndrome in a patient with primary biliary cirrhosis.
- Author:
Jun Ki MIN
1
;
Kyung Soo PARK
;
Won Jong YU
;
Youn Soo LEE
;
Sung Min PARK
;
Sung Hwan PARK
;
Chul Soo CHO
;
Ho Youn KIM
Author Information
1. Department of Internal Medicine, Catholic University Medical College, Holy Family Hospital, Kyunggi-Do, Korea.
- Publication Type:Case Report
- Keywords:
systemic mononuclear inflammatory vasculopathy;
Sjogren's syndrome;
primary biliary cirrhosis
- MeSH:
Biopsy, Needle;
Case Report;
Diagnosis, Differential;
Female;
Follow-Up Studies;
Human;
Liver Cirrhosis, Biliary/diagnosis+ACo-;
Liver Cirrhosis, Biliary/complications+ACo-;
Middle Age;
Prednisone/administration +ACY- dosage;
Sjogren's Syndrome/pathology;
Sjogren's Syndrome/diagnosis+ACo-;
Sjogren's Syndrome/complications;
Sural Nerve/pathology;
Treatment Outcome;
Vasculitis/pathology;
Vasculitis/drug therapy;
Vasculitis/diagnosis+ACo-;
Vasculitis/complications
- From:The Korean Journal of Internal Medicine
2000;15(1):89-92
- CountryRepublic of Korea
- Language:English
-
Abstract:
We report a 46-year-old woman with primary biliary cirrhosis (PBC) presenting with Sjogren's syndrome and systemic mononuclear inflammatory vasculopathy. Biopsy specimens of sural nerve showed findings consistent with vasculitic neuropathy. Perivascular inflammatory mononuclear cell infiltration was observed on muscle biopsy specimen. The findings of abdominal computed tomography and brain magnetic resonance imaging were suggestive of vasculitis. Clinical manifestations and radiologic findings were improved after high dose prednisolone therapy.
