A Case of Segmental Neurofibromatosis.
- Author:
Chan Seok OH
1
;
Jae Wook MYUNG
;
Hye Jin WOO
;
Sang Hyun CHO
Author Information
1. Department of Dermatology, College of Medicine, The Catholic University of Korea, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Segmental neurofibromatosis
- MeSH:
Adult;
Biopsy;
Cafe-au-Lait Spots;
Collagen;
Diagnosis;
Female;
Humans;
Neurofibroma;
Neurofibromatoses*;
Scalp
- From:Korean Journal of Dermatology
2002;40(7):832-834
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 30-year-old woman had localized several cutaneous neurofibromas on the scalp in a dermatomal distribution(C2). Family history was negative, and evaluation for other signs such as cafe-au-lait spots, axillary frecklings, or Lisch nodules were not revealed. Biopsy specimen showed a well-circumscribed encapsulated tumor which consists of spindle cells with elongated, wavy nuclei and thin wavy collagenous strands loosely spaced in a clear matrix as seen in the neurofibroma. The diagnosis of bilateral segmental neurofibromatosis was made on the basis of the clinical features including the distribution of the neurofibromas and the absence of the family history and the histology consistent with a neurofibroma.
