Electrophysiological findings for 106 cases with auditory neuropathy
10.3321/j.issn:1673-0860.2008.05.007
- VernacularTitle:听神经病106例听力学分析
- Author:
Ji-Bao WANG
1
;
Jia-De DUAN
;
Hai-Hua CHEN
;
Jing JIN
;
Qing-Tian LI
;
Xiang HUANG
;
Wei-Jia KONG
Author Information
1. 华中科技大学同济医学院附属协和医院
- Keywords:
Vestibulocochlear nerve diseases;
Audiometry,pure-tone;
Evoked potentials,auditory brain stem
- From:
Chinese Journal of Otorhinolaryngology Head and Neck Surgery
2008;43(5):347-350
- CountryChina
- Language:Chinese
-
Abstract:
Objective To analyses the clinical characteristics and electrophysiologieal finding of 106 patients with auditory neuropathy (AN).Investigate the differencial curve type of pure tone audiogram and the abnormal ABR.Methods Review the history of patients,pure tone audiometry,middle ear acoustic reflexes,auditory brainstem response,distortion product otoacoustic emission and radiologic imaging studies of the brain of 106 patients with AN during December 2001 to May 2007 in retrospect.Results The 106 patients with AN were of both genders.The age were between 11-37 years old.and the average age was 17.5 years old.The most patients were adolescences(70.8%).Twelve cases of the 106 patients had evidence of other peripheral neuropathy in addition to hearing loss.Another 94 patients were idiopathic origins.The pure tone audiogram showed a minimal to moderate sensorineural hearing loss at low frequencies 0.5 kHz and 0.25 kHz in 209 errs(98.6%).The average hearing threshold(WHO 1997)in 23.2% of disordered ears at less than 25 dB in the "normal" range.Auditory brainstem response could not be recorded in 124 ears (58.5%) at maximum stimulus.The other 88 ears showed lor 2 wave,but the wave were small.There were 23 patients which one side ear ABR was 1 or 2 small waves presented.but the contralateral side were all waves absent.In 3 cases of AN with other peripheral neuropathy which ABR were both ears 1 or 2 small wave ear recorded.However,1 patient in our sample could not be detected distortion product otoacoustic emission at 3-6 kHz(left ear) and 5-6 kHz(right ear).Conclusions AN was not rare in adolescences.The average hearing threshold for AN should be discussed.