Diagnosis and Treatment of Erdheim-Chester Disease -Review.
10.7534/j.issn.1009-2137.2016.04.055
- Author:
Jing-Shi WANG
1
;
Zhao WANG
2
Author Information
1. Department of Hematology, Beijing Friendship Hospital Affiliated to Capital Medical University, Beijing 100050, China.
2. Department of Hematology, Beijing Friendship Hospital Affiliated to Capital Medical University, Beijing 100050, China.E-mail: zhaowww263@yahoo.com.
- Publication Type:Journal Article
- MeSH:
Erdheim-Chester Disease;
Humans
- From:
Journal of Experimental Hematology
2016;24(4):1256-1259
- CountryChina
- Language:Chinese
-
Abstract:
Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. The etiology of ECD is unknown yet. The disease is characterized by the infiltration of lipid-laden histiocytes with foamy to bones and various organs. The heterogeneous manifestations of ECD vary among different individuals. This results in a presentation that may vary from an indolent focal disease to a life threatening organ failure. This review focuses on the etiology, clinical presentation, diagnostic criteria and treatment of Erdheim-Chester disease (ECD).
