A case of primary biliary cirrhosis manifestated with idiopathic thrombocytopenic purpura and Sjogren's syndrome.
- Author:
Tae Wook WOO
1
;
Byung Ho KIM
;
Jaejun SHIM
;
Youn Hwa KIM
;
Kyung Sam CHO
Author Information
1. Department of Internal Medicine, School of Medicine, Kyung Hee University, Seoul, Korea. kimbh@khmc.or.kr
- Publication Type:Case Report
- Keywords:
Primary biliary cirrhosis;
Idiopathic thrombocytopenic purpura;
Sjogren's syndrome
- MeSH:
Aged;
Female;
Humans;
Korea;
Liver Cirrhosis, Biliary*;
Purpura, Thrombocytopenic, Idiopathic*;
Sjogren's Syndrome*
- From:Korean Journal of Medicine
2004;66(1):80-85
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary biliary cirrhosis (PBC) is rare in Korea. Although its pathogenesis is not fully understood, immunologic dysregulation is suspected because it is frequently associated with other immunologic disorders. A few cases of primary biliary cirrhosis associated with idiopathic thrombocytopenic purpura (ITP) has previously been reported. However, PBC associated with ITP and Sjogren's syndrome simultaenously has not been reported yet. We experienced a 72-year-old woman had been finally diagnosed as PBC, ITP and Sjogren's syndrome. To the best of our knowledge, this is the first case in the world. We report this case with review of related literature.
