A Case of Periumbilical Perforating Pseudoxanthoma Elasticum.
- Author:
Hyung Dong KIM
1
;
Joon PARK
;
Sung Yul LEE
;
Jong Suk LEE
;
Moon Kyun CHO
;
Yong Lip PARK
;
Kyu Uang WHANG
;
Eui Han KIM
Author Information
1. Department of Dermatology, College of Medicine, Soonchunhyang University, Seoul, Korea. topdoctor@naver.com
- Publication Type:Case Report
- Keywords:
Multiparous woman;
Periumbilical perforating pseudoxanthoma elasticum
- MeSH:
Connective Tissue Diseases;
Elastic Tissue;
Female;
Humans;
Pseudoxanthoma Elasticum*
- From:Korean Journal of Dermatology
2006;44(7):884-886
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Perforating pseudoxanthoma elasticum is a rare disorder. It is an hereditary connective tissue disease involving progressive fragmentation and dystrophic calcification of elastic fibers. The localized lesions usually occur in a periumbilical location in obese, middle-aged, multiparous black women. It is characterized clinically by yellowish, lax, well-circumscribed, reticulated or cobblestoned patches or plaques of the periumbilical region. Herein, we report a case of periumbilical perforating pseudoxanthoma elasticum which occurred in an obese, multiparous woman with no signs of hereditary systemic pseudoxanthoma elasticum.
