A Case of Dermatofibrosarcoma Protuberans on the Face with Various Cutaneous Lesions.
- Author:
Hyun Chang KO
1
;
Bong Seok JANG
;
Moon Bum KIM
;
Chang Keun OH
;
Kyung Sool KWON
Author Information
1. Department of Dermatology, School of Medicine, Pusan National University, Busan, Korea. kwonks@pusan.ac.kr
- Publication Type:Case Report
- Keywords:
Dermatofibrosarcoma protuberans;
Face
- MeSH:
Adult;
Dermatofibrosarcoma*;
Dermis;
Extremities;
Female;
Forehead;
Humans
- From:Korean Journal of Dermatology
2006;44(9):1122-1125
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Dermatofibrosarcoma protuberans is a tumor of intermediate malignancy, characterized by its aggressive local growth and marked propensity to recur after surgical excision. Dermatofibrosarcoma protuberans is most frequently located on the trunk or proximal extremities and rarely occurs on the face. In most cases, the tumor initially occurs as an asymptomatic, indurated plaque that slowly increases in size, and then develops multiple firm nodules. We report a case of a 39-year-old female who presented with a 10-year history of asymptomatic, brownish and hypopigmented plaques on the right side of her upper forehead. They gradually extended downwards and erythematous nodules appeared on the superior border of pre-existing brownish plaques 8 months ago. Histopathological examination of a nodule showed spindle-shaped cells with a storiform pattern in the dermis, and that of the plaques showed a parallel pattern. The tumor cells were stained positive for CD 34 upon immunohistochemical staining.
