A Gangliocytic Paraganglioma of the Ampulla of Vater Removed by Endoscopic Resection.
10.15279/kpba.2016.21.2.87
- Author:
Jin Hee JUNG
1
;
Byung Moo YOO
;
Yoo Jin UM
;
Hundo CHO
;
Young Hwan AHN
;
Min Jae YANG
;
Jae Chul HWANG
;
Jin Hong KIM
Author Information
1. Department of Gastroenterology, Ajou University School of Medicine, Suwon, Korea. ybm6403@gmail.com
- Publication Type:Case Report
- Keywords:
Gangliocytic paraganglioma;
Ampulla of vater;
Endoscopic papillectomy
- MeSH:
Ampulla of Vater*;
Biopsy;
Duodenum;
Follow-Up Studies;
Ganglion Cysts;
Humans;
Lymph Nodes;
Neuroendocrine Tumors;
Paraganglioma*;
Recurrence;
Surgical Instruments
- From:Korean Journal of Pancreas and Biliary Tract
2016;21(2):87-91
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Gangliocytic paraganglioma (GP) is an extremely rare tumor that mostly occurs in the periampullary area of the duodenum. It is characterized by benign behavior and favorable outcomes, but sometimes shows regional lymph node dissemination. GP consist of three characteristic histological components: epithelioid, spindle, and ganglion cells. Therefore, it is often misdiagnosed as a neuroendocrine tumor when only endoscopic forceps biopsy is performed. The clinical management of GP has not yet been standardized. This case report describes an asymptomatic patient who was initially diagnosed with a grade-1 neuroendocrine tumor, but was confirmed as having benign GP after endoscopic papillectomy. Complete en-bloc resection was performed for this patient, without any significant adverse events. At a 6-month follow-up assessment, the patient remained asymptomatic and there was no evidence of recurrence.
