Treatment of Pan-craniofacial Polyostotic Fibrodysplasia not Involving Maxilla: Mandible Reconstruction with Free Fibular Bone Flap.
- Author:
Seong Jun CHEON
1
;
Kyung Suk LEE
Author Information
1. Department of Plastic and Reconstructive Surgery, College of Medicine, Gyeongsang National University, Jinju, Korea. opensound@han mail.net
- Publication Type:Original Article
- Keywords:
Fibrous dysplasia;
Mandible reconstruction;
Fibular bone free flap
- MeSH:
Congenital Abnormalities;
Fibrous Dysplasia, Polyostotic;
Free Tissue Flaps;
Humans;
Jaw;
Mandible*;
Mandibular Osteotomy;
Maxilla*;
Osteomyelitis;
Transplants;
Wound Healing
- From:Journal of the Korean Cleft Palate-Craniofacial Association
2005;6(1):69-72
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Fibrous dysplasia is a benign pathologic condition of bone and causes facial deformity as well as functional problems. The monostotic form of the disease is much more common(70-80 percent) than the polyostotic variety (20-30 percent). In craniofacial fibrous dysplasia, craniofacial involvement occurs in 10-30 percent of monostotic and 50 percent of polyostotic patients. Frontal, sphenoid, ethmoid, and maxilla bones are frequently involved. Jaw involvement may involve a solitary lesion, but nonetheless in more common in the maxilla than in the mandible. We report a case of mandible reconstruction of pan-craniofacial polyostotic fibrous dysplasia that do not involve maxilla. In operation, extensive hemimandibulectomy was done and fibular bone free flap was done for mandible reconstruction. Postoperative 6 months later, focal osteomyelitis was seen in mandible angle. We removed mini-plate and screw and illiac cancellous bone graft was performed. 3 months after second operation, wound healing was uneventful and we have a functionally and cosmetically good outcome.
