An Autopsy Case of Tracheal Agenesis Type 2.
- Author:
Hyun Joo LEE
1
;
Eun Ae PARK
;
Seung Joo LEE
;
Mi Jeong KIM
;
Soon Hee SEONG
Author Information
1. Department of Pediatrics, College of Medicine, Ewha Womans University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Respiratory distress;
Bronchoesophageal fistula;
Tracheal agenesis
- MeSH:
Aphonia;
Autopsy*;
Bronchi;
Diagnosis;
Esophagus;
Female;
Fistula;
Heart Septal Defects, Ventricular;
Humans;
Infant;
Infant, Newborn;
Intubation;
Lung;
Parturition;
Trachea
- From:Journal of the Korean Pediatric Society
1996;39(12):1759-1762
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Tracheal agenesis is the rare and uniformly lethal anomaly that presents with severe respiratory distress and aphonia after birth. In this anomaly, the trachea is usually absent and air is reaching the bronchi through a communication with the esophagus. The diagnosis should be suspected in a nowborn infant with respiratory distress whose intubation is difficult. We report an autopy case of tracheal agenesis, type 2 in a female newborn infant: Complete tracheal agenesis with the fistula between the esophagus and the carina. Associated anomalies were bilobed right lung, Meckel's divericulum and ventricular septal defect.