Acute Intermittent Porphyria and Pregnancy.
- Author:
Ji Hee RYU
1
;
Eun A CHOI
;
Hyung Min CHOI
;
Tae Yoon KIM
;
Jae Sung CHO
;
Yong Won PARK
;
Jae Wook KIM
Author Information
1. Department of Obstetrics and Gynecology, College of Medicine, Yonsei University, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Acute intermittent porphyria (AIP);
Pregnancy
- MeSH:
Biosynthetic Pathways;
Diagnosis;
Heme;
Porphyria, Acute Intermittent*;
Porphyrias;
Pregnancy*
- From:Korean Journal of Obstetrics and Gynecology
1997;40(2):414-418
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The Porphyria are a group of inherited and acquired disorders characterized by partial defects in the heme biosynthetic pathway. Among the hepatic forms, acute intermittent porphyria(AIP) is the most severe and common type in western hemisphere. Though its association with pregnancy is rare, it presents the obstetrician with challenging problems in diagnosis and management and it is probable that pregnancy had some deleterious effect in acute porphyria. The authors present a cae of AIP in pregnancy with a review of literature.
