A Case of Widespread Follicular Mucinosis in a 5-year-old Girl.
- Author:
Su Han KIM
1
;
Moon Bum KIM
;
Hyun Chang KO
;
Chang Keun OH
;
Kyung Sool KWON
Author Information
1. Department of Dermatology, School of Medicine, Pusan National University, Busan, Korea. drkmp@hanmail.net
- Publication Type:Case Report
- Keywords:
Follicular mucinosis;
Mycosis fungoides
- MeSH:
Aged;
Follow-Up Studies;
Humans;
Lymphoma;
Mucinosis, Follicular;
Mucins;
Mycosis Fungoides;
Preschool Child;
Rare Diseases
- From:Korean Journal of Dermatology
2008;46(1):147-150
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Follicular mucinosis, also known as alopecia mucinosa, is a rare disease characterized by mucinous follicular degeneration and may be accompanied by cutaneous lymphoma, particularly mycosis fungoides. Two categories of disease have been identified in patients with the benign primary form. The first occurs in younger patients with localized lesions and spontaneous regression within 2 years of the onset. The second occurs in elderly patients and shows a chronic relapsing, but benign course. In the second type, the patients are older and have widespread and infiltrated lesions that can progress to mycosis fungoides. We report a case of follicular mucinosis in a 5-year-old girl who had widely distributed lesions. We think that long-term follow-up is mandatory for the occurrence of lymphoma-associated disease.