Rapidly Progressive Interstitial Lung Disease Associated with Dermatomyositis; A Case Report.
10.4078/jkra.2007.14.4.401
- Author:
Jae Young YOON
1
;
Sun Yang MIN
;
Ju Yee PARK
;
Seung Goun HONG
;
Hyo Jong KANG
Author Information
1. Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea. joint@dmc.or.kr
- Publication Type:Case Report
- Keywords:
Interstitial lung disease;
Dermatomyositis
- MeSH:
Adult;
Cyclophosphamide;
Dermatomyositis*;
Dyspnea;
Female;
Humans;
Lung Diseases, Interstitial*;
Muscle Weakness;
Tacrolimus
- From:The Journal of the Korean Rheumatism Association
2007;14(4):401-406
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A previously healthy 44-year-old woman who was diagnosed as having dermatomyositis suddenly developed severe dyspnea while being in the state of improved condition of muscle weakness. Interstitial lung disease was found on high resolution computed tomography (HRCT). In spite of the treatment with the immune-modulating agent (high dose steroid, cyclophosphamide, immunoglubulin and cyclosporine), her condition deteriorated further and rapidly, leading to death. More intensive agent such as FK506 would be necessary in those cases of dermatomyositis-related interstitial lung disease that have poor prognostic factors.
