Mazabraud's Syndrome Coexisting with a Uterine Tumor Resembling an Ovarian Sex Cord Tumor (UTROSCT): a Case Report.
- Author:
Cuneyt CALISIR
1
;
Ulukan INAN
;
Ulas Savas YAVAS
;
Serap ISIKSOY
;
Tamer KAYA
Author Information
- Publication Type:Case Report
- Keywords: Fibrous dysplasia; Monostotic; Myxoma; Uterine neoplasms
- MeSH: Aged; Biopsy; Buttocks/pathology/surgery/ultrasonography; Diagnosis, Differential; Female; Fibrous Dysplasia, Monostotic/complications/*diagnosis/surgery; Humans; Magnetic Resonance Imaging; Myxoma/complications/*diagnosis/surgery; Ovarian Neoplasms/*diagnosis; Rare Diseases; Sex Cord-Gonadal Stromal Tumors/*diagnosis; Syndrome; Uterine Neoplasms/complications/*diagnosis/surgery
- From:Korean Journal of Radiology 2007;8(5):438-442
- CountryRepublic of Korea
- Language:English
- Abstract: The association of intramuscular myxoma and fibrous dysplasia is a rare disease known as Mazabraud's syndrome. We present a case of Mazabraud's syndrome coexisting with a uterine tumor and resembling an ovarian sex cord tumor (UTROSCT). This uterine tumor showed a high mitotic index and cytological atypia. To the best of our knowledge, the coexistence of the two different entities has not been reported in the literature.