Death of a Severe Underweight Infant with Pulmonary Interstitial Glycogenosis.
10.7580/KoreanJLegMed.2012.36.2.178
- Author:
Seon Jung JANG
1
;
Kyung Ryoul KIM
;
Hyoung Joong KIM
;
Minjung KIM
Author Information
1. Division of Forensic Medicine, National Forensic Service, Seoul, Korea. lillu79@korea.kr
- Publication Type:Case Report
- Keywords:
infant;
pulmonary interstitial glycogenosis;
underweight;
death
- MeSH:
Autopsy;
Fibrosis;
Glycogen;
Glycogen Storage Disease;
Humans;
Infant;
Inflammation;
Lung Diseases, Interstitial;
Male;
Prognosis;
Thinness
- From:Korean Journal of Legal Medicine
2012;36(2):178-181
- CountryRepublic of Korea
- Language:English
-
Abstract:
Pulmonary interstitial glycogenosis (PIG) is a very rare interstitial lung disease in infants. It is poorly understood, but its pathological features are distinct; they include uniform alveolar septal thickening, caused by a group of oval to spindle-shaped cells containing abundant glycogen, without apparent inflammation or fibrosis. PIG is usually associated with a good prognosis. However, in the present report, we describe the case of a 5-month-old male infant who died due to PIG; he was severely underweight and not administered proper treatment or care. The pathology of PIG was determined following a medico-legal autopsy.
