Malignant Fibrous Histiocytoma Originating in the Lesser Sac.
- Author:
Young Chul YUN
1
;
Kyong Hwa JUN
;
Ji Han JUNG
;
Hyung Min CHIN
;
Chung Soo CHUN
Author Information
1. Department of Surgery, St. Vincent's Hospital, The Catholic University of Korea, Korea. hchin@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Malignant fibrous histiocytoma;
Lesser sac
- MeSH:
Adult;
Extremities;
Female;
Fever;
Histiocytoma, Malignant Fibrous*;
Humans;
Middle Aged;
Paraneoplastic Syndromes;
Peritoneal Cavity*;
Prognosis;
Recurrence;
Sarcoma;
Ultrasonography
- From:Journal of the Korean Surgical Society
2005;68(6):505-508
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in adults. About 70% of tumors arise from the soft tissue of the extremities with only 12~14% of the tumors occur in the retroperitoneum. The clinical characteristics of this tumor consist of an abdominal mass, tendency for local recurrence, paraneoplastic syndrome and a poor prognosis. A 51-year-old woman was admitted to St. Vincent's Hospital with complaining of fever and an abdominal mass. Ultrasound and computed tomography revealed a huge, heterogenous mass in the lesser sac area. The patient underwent an extensive mass resection with a histologic examination revealing a MFH which was positive for alpha1- antitrypsin. We report a case of MFH presenting in the lesser sac with a review of the literatures.