Malignant Perivascular Epithelioid Cell Tumor (PEComa) Arising in the Omentum with Metastatic Peritoneal Seeding: A Case Report.
- Author:
Suk Bin JANG
1
;
Won Yong SUH
;
Ji Hyun JEON
;
Keon Woo PARK
;
Do Hyoung LIM
;
Hwan NAMGUNG
;
Soon Il LEE
Author Information
- Publication Type:Case Report
- Keywords: Perivascular epithelioid cell neoplasms; HMB-45 protein
- MeSH: Colon, Descending; Epithelioid Cells*; Humans; Korea; Liver; Middle Aged; Neoplasm Metastasis; Omentum*; Perivascular Epithelioid Cell Neoplasms; World Health Organization
- From:Korean Journal of Medicine 2014;86(1):96-101
- CountryRepublic of Korea
- Language:Korean
- Abstract: The World Health Organization (WHO) defines a perivascular epithelioid cell tumor (PEComa) as a mesenchymal neoplasia composed of perivascular epithelioid cells with characteristic morphological and immunohistochemical features. They are rarely malignant. Indeed, only a few cases have been reported in the English literature, and this is the first case of PEComa reported in Korea. A 64-year-old man presented with an abdominal mass and peritoneal seeding. The patient underwent mass excision with descending colon resection and anastomosis. The primary mass and peritoneal seeding was diagnosed as a PEComa histopathologically. Seven months later, he developed liver metastasis and aggravated peritoneal seeding. Here, we report a case of malignant PEComa of the omentum.
