Hemophagocytic Syndrome with Kawasaki Disease and Peripheral Gangrene.
- Author:
Hwa Jun YUN
1
;
Ko Woon JEON
;
Hwang Min KIM
;
Seok Won PARK
;
Young UH
Author Information
1. Department of Pediatrics, Yonsei University, Wonju College of Medicine, Wonju, Korea. khm9120@wonju.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Etoposide;
Hemophagocytic syndrome;
Bone marrow biopsy;
Kawasaki disease;
Peripheral gangrene
- MeSH:
Biopsy;
Bone Marrow;
Etoposide;
Fever;
Gangrene*;
Hepatomegaly;
Humans;
Hypertriglyceridemia;
Lymphohistiocytosis, Hemophagocytic*;
Male;
Mucocutaneous Lymph Node Syndrome*;
Thrombocytopenia
- From:Journal of the Korean Pediatric Society
2002;45(5):664-668
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A twenty six months-old boy developed hemophagocytic syndrome during the course of Kawasaki disease. Despite the appropriate treatment modalities for Kawasaki disease, he developed thrombocytopenia, hepatomegaly, high-grade fever, hypertriglyceridemia, peripheral gangrene, and evidence of hemophagocytosis in bone marrow biopsy. Although the course was stormy, he responded well to a combination therapy of corticosteroid and etoposide.
