A Case of Pulmonary Sequestration and Congenital Lobar Emphysema Presenting with Congestive Heart Failure and Pulmonary Hypertension.
- Author:
Jin Kyu KIM
1
;
I Seon KIM
;
I Seok KANG
;
Kangmo AHN
;
Heung Jae LEE
;
Jin Kook KIM
;
June HUH
Author Information
1. Department of Pediatrics, Samsung Medical Center Sungkyunkwan University School of Medicine, Seoul, Korea. herz.huh@samsung.com
- Publication Type:Case Report
- Keywords:
Pulmonary sequestration;
Emphysema;
Pulmonary hypertension;
Heart failure
- MeSH:
Arteries;
Bronchogenic Cyst;
Bronchopulmonary Sequestration;
Cystic Adenomatoid Malformation of Lung, Congenital;
Emphysema;
Estrogens, Conjugated (USP);
Heart Failure;
Humans;
Hypertension, Pulmonary;
Infant, Newborn;
Lung;
Pulmonary Emphysema
- From:Pediatric Allergy and Respiratory Disease
2009;19(4):434-439
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital cystic disease of the lung represents pulmonary sequestration, congenital lobar emphysema, bronchogenic cyst and congenital cystic adenomatoid malformation. It has a variety of clinical manifestations from immediate postnatal respiratory distress to heart failure. Pulmonary sequestration sometimes causes heart failure in neonates through a shunt between an anomalous systemic feeding artery and the pulmonary venous system. We hereby report a case with both pulmonary sequestration and congenital lobar emphysema presenting with congestive heart failure and pulmonary hypertension, which improved after lobectomy.
