Telangiectatic Focal Nodular Hyperplasia of the Liver: A Case Detected at Birth.
10.3346/jkms.2003.18.5.746
- Author:
Han Seong KIM
1
;
Young A KIM
;
Chong Jai KIM
;
Yeon Lim SUH
;
Ja June JANG
;
Je G CHI
Author Information
1. Department of Pathology, Seoul National University College of Medicine, Seoul, Korea. pathr@plaza.snu.ac.kr
- Publication Type:Case Report
- Keywords:
Telangiectasia;
Focal Nodular Hyperplasia;
Infant, Newborn;
Liver
- MeSH:
Focal Nodular Hyperplasia/*congenital/*diagnosis/radiography;
Human;
Hyperplasia;
Infant;
Liver/pathology;
Liver Neoplasms/congenital/*diagnosis/radiography;
Male;
Tomography, X-Ray Computed
- From:Journal of Korean Medical Science
2003;18(5):746-750
- CountryRepublic of Korea
- Language:English
-
Abstract:
A case of telangiectatic focal nodular hyperplasia (FNH) was detected at birth and was surgically removed. Grossly, the lesion was a solitary nodule and showed vague nodularity, appearing as an adenoma-like mass with fine fibrous septa, but having no macroscopic scar. On microscopic scale, the mass typically had neither fibrous central scar nor hyperplastic nodules different from the usual FNHs. The hepatic plates were separated by sinusoidal dilatation, sometimes alternating with areas of marked ectasia. Instead of large fibrous scar, thin fibrous septa were often found, and contained abnormal tortuous large arteries. These high-pressure vessels were connected directly into the adjacent sinusoids and made marked dilation of sinusoids. Bile ductular proliferation was also noted in the thin fibrous septa. To our knowledge, this is considered to be the first reported case of telangiectatic FNH detected at birth.
