A Case of Retroperitoneal Extrarenal Wilms' Tumor with Metastasis to Lung and Bone.
- Author:
Jea Heon JEONG
1
;
Weon Cheol HAN
;
Du Young CHOI
Author Information
1. Department of Pediatrics, School of Medicine, Wonkwang University, Iksan, Korea. cdy8118@wonkwang.ac.kr
- Publication Type:Case Report
- Keywords:
Extrarenal Wilms' tumor;
Retroperitonium
- MeSH:
Cervix Uteri;
Child;
Diagnosis;
Drug Therapy, Combination;
Female;
Humans;
Inguinal Canal;
Kidney;
Lung*;
Male;
Neoplasm Metastasis*;
Pelvic Bones;
Recurrence;
Ribs;
Skin;
Testis;
Thorax;
Uterus;
Wilms Tumor*
- From:Korean Journal of Pediatrics
2005;48(1):112-115
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Extrarenal Wilms' tumor is a very exceptional tumor which is defined as Wilms' tumor found anywhere other than in the kidneys. Until now less than 60 cases have been reported in the English literature. The tumor can be located in the retroperitoneum, inguinal canal, uterus, cervix, testes, skin and even in the thorax. The diagnosis is almost always made after surgical intervention. Distant metastasis of this tumor has only been reported in the case of a 6-year-old girl who developed Wilms' tumor in the inguinal canal with lung involvement. In this paper we report a case of extrarenal Wilms' tumor in retroperitoneum with distant metastasis to lungs, ribs and pelvic bone in a 6- year old male. The tumor was successfully removed without tumor cell spillage. The patient was diagnosed as favorable histologic group, in which the tumor consists of epithelial, blastemal and mesenchymal components without teratomatous elements. He received combination chemotherapy according to NWTS-IV guidelines and radiation to involved lungs, and has been alive and well for the last 6 months without severe complication or relapse.
