Congenital Pulmonary Vein Stenosis with Normal Anatomical Connection: One case report.
- Author:
Joonseok PARK
1
;
Yun Hee CHANG
;
Mi Jin JUNG
;
I Seok KANG
;
Tae Gook JUN
Author Information
1. Department of Thoracic and Cardiovascular Surgery, Samsung Seoul Hospital, Sungkyunkwan University School of Medicine, Korea. tgjun@smc.samsung.co.kr
- Publication Type:Case Report
- Keywords:
Pulmonary veins;
Suture;
Surgery method;
Congenital heart defect
- MeSH:
Constriction, Pathologic*;
Dilatation;
Heart Defects, Congenital;
Heart Failure;
Hypertension, Pulmonary;
Iloprost;
Lung Transplantation;
Mortality;
Pneumonectomy;
Pulmonary Veins*;
Stents;
Sutures;
Transplants;
Vasodilator Agents;
Sildenafil Citrate
- From:The Korean Journal of Thoracic and Cardiovascular Surgery
2004;37(4):364-368
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Congenital pulmonary vein stenosis is a rare anomaly and related to high mortality due to progressive pulmonary hypertension and heart failure in infancy. Aggressive anti-failure medication and surgical treatment is recommended. Surgical options are balloon dilatation, endovascular stent, pneumonectomy, lung transplantation, patch grafting, and sutureless repair. We report a case of congenital pulmonary vein stenosis with normal anatomical connection successfully treated with sutureless technique and using pulmonary vasodilators, such as Sildenafil, Iloprost and iNO postoperatively.
