Ectopic ACTH Syndrome Due to Pheochromocytoma: A case report.
10.16956/kjes.2002.2.2.116
- Author:
Suck Joon HONG
1
;
Won Bae KIM
Author Information
1. Department of Surgery, Ulsan University College of Medicine, Asan Medical Center, Korea. SJHONG2@AMC.SEOUL.kr
- Publication Type:Case Report
- Keywords:
Pheochromocytoma;
Ectopic ACTH Syndrome
- MeSH:
ACTH Syndrome, Ectopic*;
Adrenocorticotropic Hormone;
Alkalosis;
Cushing Syndrome;
Diagnosis;
Female;
Glucose Intolerance;
Humans;
Liver;
Mortality;
Pheochromocytoma*
- From:Korean Journal of Endocrine Surgery
2002;2(2):116-119
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 28-year old female was diagnosed preoperatively to have a pheochromocytoma producing ACTH at other hospital. However the operation was delayed due to poor general condition and abnormal liver function. She revealed severe hypercortisolism, hypokalemic metabolic alkalosis, glucose intolerance and showed rapid downhill course. She was transferred to our hospital for operation but septic complications were strarted already. She was not recovered in spite of desperate operation and died just after moribund discharge. ACTH producing pheochromocytoma is uncommon and literature review indicated high mortality rates due to improper preoperative diagnosis. Proper preoperative recognition and early surgical management is mandatory for better results.
