A Case of Hypertrophic Cardiomyopathy Associated with Wolff-Parkinson-White Syndrome.
- Author:
Young Joo KWON
1
;
Soon Ju LEE
;
Ju Mi KANG
;
Phil Sang JANG
;
Dong Un KIM
;
Keun Young LEE
;
Young Hoon KIM
;
Jin Tack KIM
Author Information
1. Department of Pediatrics, College of Medicine, The Catholic University of Korea, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Wolff-Parkinson-White Syndrome;
Hypertrophic cardiomyopathy;
Sudden cardiac death;
Hydrocephalus
- MeSH:
Adolescent;
Cardiomyopathy, Hypertrophic*;
Death, Sudden;
Death, Sudden, Cardiac;
Heart Ventricles;
Humans;
Hydrocephalus;
Hypertrophy;
Myocardium;
Prevalence;
Tachycardia;
Wolff-Parkinson-White Syndrome*;
Young Adult
- From:Journal of the Korean Pediatric Cardiology Society
2004;8(1):181-186
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hypertrophic cardiomyopathy(HCM) is defined as a thickened wall of heart muscles and non-dilated left ventricle, but is not accompanied underlying cardiac or systemic diseases that induce ventricular hypertrophy. HCM is responsible to exercise limitation for all ages and also is known as the most common cause of heart-related sudden death during childhood and adolescents. Epidemiological studies showed that prevalence in young adults is 0.2% and HCM is caused by a mutations in genes that code the proteins of cardiac muscles. HCM with Wolff-Parkinson-White Syndrome is extremely rare and associated with a high risk of tachyarrhythmia and sudden death. We report an infantile HCM with WPW syndrome who died suddenly.
