Creutzfeldt-jakob disease.
- Author:
O Hyoun KWON
1
;
Duk L NA
;
Jung Il LEE
;
Yeon Lim SUH
;
Dae Won SEO
;
Sang Eun KIM
;
Bong Ae WIE
Author Information
1. Department of Neurology, Samsung Medical Center.
- Publication Type:Original Article
- MeSH:
Cerebellar Diseases;
Creutzfeldt-Jakob Syndrome*;
Dyskinesias;
Electroencephalography;
Magnetic Resonance Imaging;
Positron-Emission Tomography;
Strikes, Employee
- From:Journal of the Korean Neurological Association
1997;15(1):137-151
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
We present three neuropathologically-verified and two clinically-probable cases of Creutfeldt Jakob disease. All five had nonspecific prodromal complaints or symptoms prior to overt neurological signs and showed striking progressive neurologic deterioration, especially cognitive decline and cerebellar dysfunction. Myoclonic involuntary movements and complete decapitated states followed in one or two months. The characteristic even pathognomonic in proper clinical settings, features of electroencephalography, magnetic resonance imaging and positron emission tomography and pathologic findings are presented.