A Case of Primary Cutaneous Anaplastic Large Cell Lymphoma with Extensive Limb Disease.
10.3904/kjm.2015.89.3.353
- Author:
Jae Ho BYEON
1
;
In Sook WOO
;
Won Jik LEE
;
Sung Hee KAM
;
Chi Wha HAN
;
Yun Hwa JUNG
Author Information
1. Division of Hematology-Oncology, Department of Internal Medicine, Yeouido St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea. ksdmz@hanmail.net
- Publication Type:Case Report
- Keywords:
Lymphoma;
Primary cutaneous anaplastic large cell
- MeSH:
Drug Therapy;
Extremities*;
Lymphoma;
Lymphoma, Non-Hodgkin;
Lymphoma, Primary Cutaneous Anaplastic Large Cell*;
Prognosis;
Skin;
Survival Rate
- From:Korean Journal of Medicine
2015;89(3):353-357
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primary cutaneous anaplastic large cell lymphoma (pcALCL) is a rare subtype of malignant non-Hodgkin lymphoma, in which 40% of the cases show spontaneous regression without aggressive treatment. Surgery and focal radiation therapy are the primary forms of treatment for this disease; however, if pcALCL is accompanied by multifocal skin lesions, chemotherapy is also common. The prognosis for pcALCL is generally excellent, with a 5-year survival rate of 85-100%. However, pcALCL with extensive limb disease typically has a poor prognosis. Here, we present a case of pcALCL with extensive limb disease that resulted in the patient's death, despite the use of aggressive chemotherapy.
