A Case of Poland Syndrome with Diabetic Ketoacidosis.
- Author:
Su Mi IN
1
;
Hyoung Shin LEE
;
Jae Hong YU
Author Information
1. Department of Pediatrics, College of Medicine, Chungnam National University, Taejon, Korea. jhongyu@cuvic.cnu.ac.kr
- Publication Type:Case Report
- Keywords:
Poland syndrome;
Diabetic ketoacidosis
- MeSH:
Adolescent;
Diabetes Mellitus;
Diabetic Ketoacidosis*;
Female;
Humans;
Incidence;
Ketosis;
Pectoralis Muscles;
Poland Syndrome*;
Poland*;
Syndactyly;
Upper Extremity
- From:Journal of Korean Society of Pediatric Endocrinology
2000;5(1):127-131
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Poland syndrome is characterized by an absent of the pectoralis major muscle, with ipsilateral defect of the upper extremity, usually syndactyly. The incidence of this syndrome has been estimated at 1 per 32,000 persons and more than 400 patients have been described worldwide after Alfred Poland's report. but there was no report of Poland syndrome associated with Diabetic Mellitus in childhood. Recently, we experienced a 14 year-old female patient who showed typical Poland syndrome, a left pectoralis muscle hypoplasia and left synbrachydactyly, associated with Diabetes mellitus complicated by ketoacidosis.
